Names & Taxonomy

Uniprot ID:
P51649
Entry Name:
SSDH_HUMAN
Status:
reviewed
Protein Names:
Succinate-semialdehyde dehydrogenase, mitochondrial (EC 1.2.1.24) (Aldehyde dehydrogenase family 5 member A1) (NAD(+)-dependent succinic semialdehyde dehydrogenase)
Gene Names:
ALDH5A1 SSADH
Gene Names Primary:
ALDH5A1
Organism:
Homo sapiens (Human)

Structure

Length:
535
Sequence:
MATCIWLRSCGARRLGSTFPGCRLRPRAGGLVPASGPAPGPAQLRCYAGRLAGLSAALLRTDSFVGGRWLPAAATFPVQDPASGAALGMVADCGVREARAAVRAAYEAFCRWREVSAKERSSLLRKWYNLMIQNKDDLARIITAESGKPLKEAHGEILYSAFFLEWFSEEARRVYGDIIHTPAKDRRALVLKQPIGVAAVITPWNFPSAMITRKVGAALAAGCTVVVKPAEDTPFSALALAELASQAGIPSGVYNVIPCSRKNAKEVGEAICTDPLVSKISFTGSTTTGKILLHHAANSVKRVSMELGGLAPFIVFDSANVDQAVAGAMASKFRNTGQTCVCSNQFLVQRGIHDAFVKAFAEAMKKNLRVGNGFEEGTTQGPLINEKAVEKVEKQVNDAVSKGATVVTGGKRHQLGKNFFEPTLLCNVTQDMLCTHEETFGPLAPVIKFDTEEEAIAIANAADVGLAGYFYSQDPAQIWRVAEQLEVGMVGVNEGLISSVECPFGGVKQSGLGREGSKYGIDEYLELKYVCYGGL
Proteomes:
UP000005640

Subcellular location

Subcellular Location:
Mitochondrion.

Function

Function:
Catalyzes one step in the degradation of the inhibitory neurotransmitter gamma-aminobutyric acid (GABA).
Pathway:
Amino-acid degradation; 4-aminobutanoate degradation.
Catalytic Activity:
Succinate semialdehyde + NAD(+) + H(2)O = succinate + NADH.
Enzyme Regulation:
ENZYME REGULATION: Redox-regulated. Inhibited under oxydizing conditions. Inhibited by hydrogen peroxide H(2)O(2).
Active Site:
ACT_SITE 306 306 Proton acceptor.
Cross Reference Drug Bank:
DB00534 DB00139 DB00313
Gene Ontology Go:
mitochondrial matrix
mitochondrion
presynapse
aldehyde dehydrogenase (NAD) activity
carboxylic acid binding
NAD binding
protein homodimerization activity
succinate-semialdehyde dehydrogenase (NAD+) activity
succinate-semialdehyde dehydrogenase activity
acetate metabolic process
central nervous system development
galactosylceramide metabolic process
gamma-aminobutyric acid catabolic process
glucose metabolic process
glucosylceramide metabolic process
glutamate metabolic process
glutamine metabolic process
glutathione metabolic process
glycerophospholipid metabolic process
neurotransmitter catabolic process
neurotransmitter secretion
post-embryonic development
protein homotetramerization
respiratory electron transport chain
short-chain fatty acid metabolic process
succinate metabolic process
synaptic transmission
Gene Ontology Biological Process:
acetate metabolic process
central nervous system development
galactosylceramide metabolic process
gamma-aminobutyric acid catabolic process
glucose metabolic process
glucosylceramide metabolic process
glutamate metabolic process
glutamine metabolic process
glutathione metabolic process
glycerophospholipid metabolic process
neurotransmitter catabolic process
neurotransmitter secretion
post-embryonic development
protein homotetramerization
respiratory electron transport chain
short-chain fatty acid metabolic process
succinate metabolic process
synaptic transmission
Gene Ontology Molecular Function:
aldehyde dehydrogenase (NAD) activity
carboxylic acid binding
NAD binding
protein homodimerization activity
succinate-semialdehyde dehydrogenase (NAD+) activity
succinate-semialdehyde dehydrogenase activity
Gene Ontology Cellular Component:
mitochondrial matrix
mitochondrion
presynapse
Keywords:
3D-structure
Acetylation
Alternative splicing
Complete proteome
Disease mutation
Disulfide bond
Mitochondrion
NAD
Oxidoreductase
Phosphoprotein
Polymorphism
Reference proteome
Transit peptide

Publication

PubMed ID:
9683595 12208142 14702039 14574404 15489334 7814412 9059628 19608861 21269460 24275569 19300440 11243727 11901270 14635103