Names & Taxonomy
- Uniprot ID:
- P30084
- Entry Name:
- ECHM_HUMAN
- Status:
- reviewed
- Protein Names:
- Enoyl-CoA hydratase, mitochondrial (EC 4.2.1.17) (Enoyl-CoA hydratase 1) (Short-chain enoyl-CoA hydratase) (SCEH)
- Gene Names:
- ECHS1
- Gene Names Primary:
- ECHS1
- Organism:
- Homo sapiens (Human)
Structure
- Length:
- 290
- Sequence:
- MAALRVLLSCVRGPLRPPVRCPAWRPFASGANFEYIIAEKRGKNNTVGLIQLNRPKALNALCDGLIDELNQALKTFEEDPAVGAIVLTGGDKAFAAGADIKEMQNLSFQDCYSSKFLKHWDHLTQVKKPVIAAVNGYAFGGGCELAMMCDIIYAGEKAQFAQPEILIGTIPGAGGTQRLTRAVGKSLAMEMVLTGDRISAQDAKQAGLVSKICPVETLVEEAIQCAEKIASNSKIVVAMAKESVNAAFEMTLTEGSKLEKKLFYSTFATDDRKEGMTAFVEKRKANFKDQ
- Proteomes:
- UP000005640
Subcellular location
- Subcellular Location:
- Mitochondrion matrix.
Function
- Function:
- Straight-chain enoyl-CoA thioesters from C4 up to at least C16 are processed, although with decreasing catalytic rate.
- Pathway:
- Lipid metabolism; fatty acid beta-oxidation.
- Catalytic Activity:
- (3S)-3-hydroxyacyl-CoA = trans-2(or 3)-enoyl-CoA + H(2)O.
- Gene Ontology Go:
- extracellular exosome
mitochondrial matrix
mitochondrion
enoyl-CoA hydratase activity
cellular lipid metabolic process
fatty acid beta-oxidation
small molecule metabolic process - Gene Ontology Biological Process:
- cellular lipid metabolic process
fatty acid beta-oxidation
small molecule metabolic process - Gene Ontology Molecular Function:
- enoyl-CoA hydratase activity
- Gene Ontology Cellular Component:
- extracellular exosome
mitochondrial matrix
mitochondrion - Keywords:
- 3D-structure
Acetylation
Complete proteome
Direct protein sequencing
Disease mutation
Fatty acid metabolism
Lipid metabolism
Lyase
Mitochondrion
Neurodegeneration
Phosphoprotein
Polymorphism
Reference proteome
Transit peptide - Interacts With:
- Q5S007; P40763; P42227