Names & Taxonomy
- Uniprot ID:
- Q7KZA3
- Entry Name:
- Q7KZA3_HUMAN
- Status:
- unreviewed
- Protein Names:
- Ferrochelatase (EC 4.99.1.1)
- Gene Names:
- DKFZp686P18130
- Gene Names Primary:
- DKFZp686P18130
- Organism:
- Homo sapiens (Human)
Structure
- Length:
- 416
- Sequence:
- MAAALRAAGVLLRDPLASSSWRVCQPWRWKSGAAAAAVTTETAQHAQGAKPQVQPQKRKPKTGILMLNMGGPETLGDVHDFLLRLFLDRDLMTLPIQNKLAPFIAKRRTPKIQEQYRRIGGGSPIKIWTSKQGEGMVKLLDELSPNTAPHKYYIGFRYVHPLTEEAIEEMERDGLERAIAFTQYPQYSCSTTGSSLNAIYRYYNQVGRKPTMKWSTIDRWPTHHLLIQCFADHILKELDHFPLEKRSEVVILFSAHSLPMSVVNRGDPYPQEVSATVQKVMERLEYCNPYRLVWQSKVGPMPWLGPQTDESIKGLCERGRKNILLVPIAFTSDHIETLYELDIEYSQVLAKECGVENIRRAESLNGNPLFSKALADLVHSHIQSNELCSKQLTLSCPLCVNPVCRETKSFFTSQQL
Function
- Function:
- Catalyzes the ferrous insertion into protoporphyrin IX.
- Pathway:
- Porphyrin-containing compound metabolism; protoheme biosynthesis; protoheme from protoporphyrin-IX: step 1/1.
- Catalytic Activity:
- Protoheme + 2 H(+) = protoporphyrin + Fe(2+).
- Cross Reference Drug Bank:
- DB02659
- Gene Ontology Go:
- ferrochelatase activity
heme biosynthetic process - Gene Ontology Biological Process:
- heme biosynthetic process
- Gene Ontology Molecular Function:
- ferrochelatase activity
- Keywords:
- Heme biosynthesis
Iron
Lyase
Porphyrin biosynthesis