Names & Taxonomy

Uniprot ID:
Q14353
Entry Name:
GAMT_HUMAN
Status:
reviewed
Protein Names:
Guanidinoacetate N-methyltransferase (EC 2.1.1.2)
Gene Names:
GAMT
Gene Names Primary:
GAMT
Organism:
Homo sapiens (Human)

Structure

Length:
236
Sequence:
MSAPSATPIFAPGENCSPAWGAAPAAYDAADTHLRILGKPVMERWETPYMHALAAAASSKGGRVLEVGFGMAIAASKVQEAPIDEHWIIECNDGVFQRLRDWAPRQTHKVIPLKGLWEDVAPTLPDGHFDGILYDTYPLSEETWHTHQFNFIKNHAFRLLKPGGVLTYCNLTSWGELMKSKYSDITIMFEETQVPALLEAGFRRENIRTEVMALVPPADCRYYAFPQMITPLVTKG
Proteomes:
UP000005640

Function

Function:
Converts guanidinoacetate to creatine, using S-adenosylmethionine as the methyl donor (PubMed:26003046, PubMed:24415674, PubMed:26319512). Important in nervous system development (PubMed:24415674).
Pathway:
Amine and polyamine biosynthesis; creatine biosynthesis; creatine from L-arginine and glycine: step 2/2.
Catalytic Activity:
S-adenosyl-L-methionine + guanidinoacetate = S-adenosyl-L-homocysteine + creatine.
Cross Reference Drug Bank:
DB00148 DB00536
Gene Ontology Go:
cytoplasm
cytosol
extracellular exosome
nucleus
guanidinoacetate N-methyltransferase activity
methyltransferase activity
cellular nitrogen compound metabolic process
creatine biosynthetic process
creatine metabolic process
embryonic liver development
muscle contraction
organ morphogenesis
polyamine metabolic process
regulation of multicellular organism growth
S-adenosylhomocysteine metabolic process
S-adenosylmethionine metabolic process
small molecule metabolic process
spermatogenesis
Gene Ontology Biological Process:
cellular nitrogen compound metabolic process
creatine biosynthetic process
creatine metabolic process
embryonic liver development
muscle contraction
organ morphogenesis
polyamine metabolic process
regulation of multicellular organism growth
S-adenosylhomocysteine metabolic process
S-adenosylmethionine metabolic process
small molecule metabolic process
spermatogenesis
Gene Ontology Molecular Function:
guanidinoacetate N-methyltransferase activity
methyltransferase activity
Gene Ontology Cellular Component:
cytoplasm
cytosol
extracellular exosome
nucleus
Keywords:
3D-structure
Acetylation
Alternative splicing
Complete proteome
Disease mutation
Methyltransferase
Polymorphism
Reference proteome
S-adenosyl-L-methionine
Transferase

Publication

PubMed ID:
8547310 9325156 14702039 15057824 15489334 8651275 21269460 22223895 12468279 15108290 15651030 16293431 16855203 17101918 17466557 19388150 23660394 24415674 26003046 26319512