Names & Taxonomy

Uniprot ID:
H7C400
Entry Name:
H7C400_HUMAN
Status:
unreviewed
Protein Names:
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (EC 3.1.2.4) (3-hydroxyisobutyryl-coenzyme A hydrolase) (Fragment)
Gene Names:
HIBCH
Gene Names Primary:
HIBCH
Organism:
Homo sapiens (Human)

Structure

Length:
52
Sequence:
DVGGGYFLPRLQGKLGYFLALTGFRLKGRDVYRAGIATHFVDSEKNGDDTIT
Proteomes:
UP000005640

Subcellular location

Subcellular Location:
Mitochondrion

Function

Function:
Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite.
Pathway:
Amino-acid degradation; L-valine degradation.
Catalytic Activity:
3-hydroxy-2-methylpropanoyl-CoA + H(2)O = CoA + 3-hydroxy-2-methylpropanoate.
Gene Ontology Go:
hydro-lyase activity
Gene Ontology Molecular Function:
hydro-lyase activity
Keywords:
Branched-chain amino acid catabolism
Complete proteome
Hydrolase
Mitochondrion
Proteomics identification
Reference proteome
Transit peptide

Publication

PubMed ID:
15815621 21269460 24275569 25944712