Names & Taxonomy
- Uniprot ID:
- H7C400
- Entry Name:
- H7C400_HUMAN
- Status:
- unreviewed
- Protein Names:
- 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (EC 3.1.2.4) (3-hydroxyisobutyryl-coenzyme A hydrolase) (Fragment)
- Gene Names:
- HIBCH
- Gene Names Primary:
- HIBCH
- Organism:
- Homo sapiens (Human)
Structure
- Length:
- 52
- Sequence:
- DVGGGYFLPRLQGKLGYFLALTGFRLKGRDVYRAGIATHFVDSEKNGDDTIT
- Proteomes:
- UP000005640
Subcellular location
- Subcellular Location:
- Mitochondrion
Function
- Function:
- Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite.
- Pathway:
- Amino-acid degradation; L-valine degradation.
- Catalytic Activity:
- 3-hydroxy-2-methylpropanoyl-CoA + H(2)O = CoA + 3-hydroxy-2-methylpropanoate.
- Gene Ontology Go:
- hydro-lyase activity
- Gene Ontology Molecular Function:
- hydro-lyase activity
- Keywords:
- Branched-chain amino acid catabolism
Complete proteome
Hydrolase
Mitochondrion
Proteomics identification
Reference proteome
Transit peptide