Names & Taxonomy

Uniprot ID:
B1AHL2
Entry Name:
B1AHL2_HUMAN
Status:
unreviewed
Protein Names:
Fibulin-1
Gene Names:
FBLN1
Gene Names Primary:
FBLN1
Organism:
Homo sapiens (Human)

Structure

Length:
721
Sequence:
MERAAPSRRVPLPLLLLGGLALLAAGVDADVLLEACCADGHRMATHQKDCSLPYATESKECRAVGLASLCQDLNGAWAVWKVGRASQAEGTASARAQRRGMVQEQCCHSQLEELHCATGISLANEQDRCATPHGDNASLEATFVKRCCHCCLLGRAAQAQGQSCEYSLMVGYQCGQVFQACCVKSQETGDLDVGGLQETDKIIEVEEEQEDPYLNDRCRGGGPCKQQCRDTGDEVVCSCFVGYQLLSDGVSCEDVNECITGSHSCRLGESCINTVGSFRCQRDSSCGTGYELTEDNSCKDIDECESGIHNCLPDFICQNTLGSFRCRPKLQCKSGFIQDALGNCIDINECLSISAPCPIGHTCINTEGSYTCQKNVPNCGRGYHLNEEGTRCVDVDECAPPAEPCGKGHRCVNSPGSFRCECKTGYYFDGISRMCVDVNECQRYPGRLCGHKCENTLGSYLCSCSVGFRLSVDGRSCEDINECSSSPCSQECANVYGSYQCYCRRGYQLSDVDGVTCEDIDECALPTGGHICSYRCINIPGSFQCSCPSSGYRLAPNGRNCQDIDECVTGIHNCSINETCFNIQGGFRCLAFECPENYRRSAATRCERLPCHENRECSKLPLRITYYHLSFPTNIQAPAVVFRMGPSSAVPGDSMQLAITGGNEEGFFTTRKVSPHSGVVALTKPVPEPRDLLLTVKMDLSRHGTVSSFVAKLFIFVSAEL
Proteomes:
UP000005640

Subcellular location

Subcellular Location:
Secreted, extracellular space, extracellular matrix

Function

Function:
Incorporated into fibronectin-containing matrix fibers. May play a role in cell adhesion and migration along protein fibers within the extracellular matrix (ECM). Could be important for certain developmental processes and contribute to the supramolecular organization of ECM architecture, in particular to those of basement membranes.
Gene Ontology Go:
proteinaceous extracellular matrix
calcium ion binding
peptidase activator activity
extracellular matrix organization
Gene Ontology Biological Process:
extracellular matrix organization
Gene Ontology Molecular Function:
calcium ion binding
peptidase activator activity
Gene Ontology Cellular Component:
proteinaceous extracellular matrix
Keywords:
Calcium
Complete proteome
Disulfide bond
EGF-like domain
Extracellular matrix
Proteomics identification
Reference proteome
Repeat
Secreted
Signal

Publication

PubMed ID:
10591208 24275569