Names & Taxonomy
- Uniprot ID:
- Q9NUT2
- Entry Name:
- ABCB8_HUMAN
- Status:
- reviewed
- Protein Names:
- ATP-binding cassette sub-family B member 8, mitochondrial (Mitochondrial ATP-binding cassette 1) (M-ABC1)
- Gene Names:
- ABCB8 MABC1
- Gene Names Primary:
- ABCB8
- Organism:
- Homo sapiens (Human)
Structure
- Length:
- 735
- Sequence:
- MLVHLFRVGIRGGPFPGRLLPPLRFQTFSAVRNTWRNGKTGQLHKAEGEYSDGYRSSSLLRAVAHLRSQLWAHLPRAPLAPRWSPSAWCWVGGALLGPMVLSKHPHLCLVALCEAEEAPPASSTPHVVGSRFNWKLFWQFLHPHLLVLGVAVVLALGAALVNVQIPLLLGQLVEVVAKYTRDHVGSFMTESQNLSTHLLILYGVQGLLTFGYLVLLSHVGERMAVDMRRALFSSLLRQDITFFDANKTGQLVSRLTTDVQEFKSSFKLVISQGLRSCTQVAGCLVSLSMLSTRLTLLLMVATPALMGVGTLMGSGLRKLSRQCQEQIARAMGVADEALGNVRTVRAFAMEQREEERYGAELEACRCRAEELGRGIALFQGLSNIAFNCMVLGTLFIGGSLVAGQQLTGGDLMSFLVASQTVQRSMANLSVLFGQVVRGLSAGARVFEYMALNPCIPLSGGCCVPKEQLRGSVTFQNVCFSYPCRPGFEVLKDFTLTLPPGKIVALVGQSGGGKTTVASLLERFYDPTAGVVMLDGRDLRTLDPSWLRGQVVGFISQEPVLFGTTIMENIRFGKLEASDEEVYTAAREANAHEFITSFPEGYNTVVGERGTTLSGGQKQRLAIARALIKQPTVLILDEATSALDAESERVVQEALDRASAGRTVLVIAHRLSTVRGAHCIVVMADGRVWEAGTHEELLKKGGLYAELIRRQALDAPRTAAPPPKKPEGPRSHQHKS
- Proteomes:
- UP000005640
Subcellular location
- Subcellular Location:
- Mitochondrion inner membrane
Function
- Cross Reference Drug Bank:
- DB00997
- Gene Ontology Go:
- ATP-binding cassette (ABC) transporter complex
membrane
mitochondrial envelope
mitochondrial inner membrane
mitochondrion
nucleolus
nucleus
ATP binding
ATPase activity, coupled to transmembrane movement of substances
transporter activity
transmembrane transport
transport - Gene Ontology Biological Process:
- transmembrane transport
transport - Gene Ontology Molecular Function:
- ATPase activity, coupled to transmembrane movement of substances
ATP binding
transporter activity - Gene Ontology Cellular Component:
- ATP-binding cassette (ABC) transporter complex
membrane
mitochondrial envelope
mitochondrial inner membrane
mitochondrion
nucleolus
nucleus - Keywords:
- ATP-binding
Alternative splicing
Complete proteome
Membrane
Mitochondrion
Mitochondrion inner membrane
Nucleotide-binding
Polymorphism
Reference proteome
Transit peptide
Transmembrane
Transmembrane helix
Transport