Names & Taxonomy

Uniprot ID:
Q96RQ9
Entry Name:
OXLA_HUMAN
Status:
reviewed
Protein Names:
L-amino-acid oxidase (LAAO) (LAO) (EC 1.4.3.2) (Interleukin-4-induced protein 1) (IL4-induced protein 1) (Protein Fig-1) (hFIG1)
Gene Names:
IL4I1 FIG1 UNQ636/PRO1265
Gene Names Orf:
UNQ636/PRO1265
Gene Names Primary:
IL4I1
Organism:
Homo sapiens (Human)

Structure

Length:
567
Sequence:
MAPLALHLLVLVPILLSLVASQDWKAERSQDPFEKCMQDPDYEQLLKVVTWGLNRTLKPQRVIVVGAGVAGLVAAKVLSDAGHKVTILEADNRIGGRIFTYRDQNTGWIGELGAMRMPSSHRILHKLCQGLGLNLTKFTQYDKNTWTEVHEVKLRNYVVEKVPEKLGYALRPQEKGHSPEDIYQMALNQALKDLKALGCRKAMKKFERHTLLEYLLGEGNLSRPAVQLLGDVMSEDGFFYLSFAEALRAHSCLSDRLQYSRIVGGWDLLPRALLSSLSGLVLLNAPVVAMTQGPHDVHVQIETSPPARNLKVLKADVVLLTASGPAVKRITFSPPLPRHMQEALRRLHYVPATKVFLSFRRPFWREEHIEGGHSNTDRPSRMIFYPPPREGALLLASYTWSDAAAAFAGLSREEALRLALDDVAALHGPVVRQLWDGTGVVKRWAEDQHSQGGFVVQPPALWQTEKDDWTVPYGRIYFAGEHTAYPHGWVETAVKSALRAAIKINSRKGPASDTASPEGHASDMEGQGHVHGVASSPSHDLAKEEGSHPPVQGQLSLQNTTHTRTSH
Proteomes:
UP000005640

Subcellular location

Subcellular Location:
Isoform 1: Lysosome

Function

Function:
Lysosomal L-amino-acid oxidase with highest specific activity with phenylalanine. May play a role in lysosomal antigen processing and presentation (By similarity).
Catalytic Activity:
An L-amino acid + H(2)O + O(2) = a 2-oxo acid + NH(3) + H(2)O(2).
Cofactor:
COFACTOR: Name=FAD; Xref=ChEBI:CHEBI:57692;
Cross Reference Drug Bank:
DB03147
Gene Ontology Go:
extracellular region
lysosome
L-amino-acid oxidase activity
cellular nitrogen compound metabolic process
L-phenylalanine catabolic process
small molecule metabolic process
Gene Ontology Biological Process:
cellular nitrogen compound metabolic process
L-phenylalanine catabolic process
small molecule metabolic process
Gene Ontology Molecular Function:
L-amino-acid oxidase activity
Gene Ontology Cellular Component:
extracellular region
lysosome
Keywords:
3D-structure
Alternative promoter usage
Alternative splicing
Complete proteome
Direct protein sequencing
Disulfide bond
FAD
Flavoprotein
Glycoprotein
Lysosome
Oxidoreductase
Polymorphism
Reference proteome
Signal

Publication

PubMed ID:
12031486 16029492 12975309 15489334 15340161 19159218 25944712